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Tag Archives: PKU

Back-to-School – Talking to Teachers About PKU

It’s Back-to-School Time! 

back-to-school-imageThe return to school is an exciting time of year.  But for a parent of a child with a metabolic disorder, such as Phenylketonuria (PKU), there are also certain concerns and stresses that comes with the start of school. 

Each year you may be faced with educating a new teacher or school nurse about PKU.

What is PKU?  

How it is Treated?  

What that means to the teacher…

Nutricia Metabolics is proud to share an educational handout to help you inform your child’s new teacher and/or school nurse about PKU.

It includes information about What PKU is, What happens, How it is treated with additional classroom tips for the teacher.

Click to Download:  Guide to PKU – Teachers & School Nurses

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Click to Download

Looking for a School Friendly PKU Formula?

Back-to-School with Periflex LQ - TEENS

Try Periflex®LQ – Request a Sample Now

Make PKU Formula Part of Your Daily Routine

If you have Phenylketonuria (PKU), then you know PKU formula is part of your life.  

PKU Formula is one of the most important parts of your diet.

Since PKU is generally managed with a diet low in whole protein, you need to get additional, PKU-appropriate protein from a different source.

PKU formula is your main source of protein and is essential for your health and well-being. Taking your full prescription of formula every day will provide your body with the protein it needs.

 

Here are some tips to help make PKU formula part of your daily routine
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Learn more about Why you need PKU Formula with these tips for Making PKU Formula Part of your Routine 

Download Now

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Create a Custom GMP-based PKU formula!

Have you wish you could turn your favorite drink to a great tasting PKU formula?

NOW YOU CAN!

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Introducing…PhenylAde® GMP Mix-In 

 

  • An easy way to add Glycomacropeptide (GMP), made from a whole protein source, to your PKU diet

  • Simply mix with just 6 fl oz of water or any flavored drink for added variety

  • Great as a once daily or as your main PKU formula*

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So many choices, how will you mix it in?

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*Must be combined with an appropriate vitamin and mineral supplement when taken as the sole source of PKU medical food.   Be sure to consult your metabolic healthcare professional prior to making any changes to your PKU diet plan.

Available is US only.

Request A Sample

What is PKU?

What is PKU?

PKU is short for Phenyketonuria. PKU is a genetic disorder that a child inherits from both parents. For a child to be born with PKU both parents must either be carriers of PKU or have PKU, which means they carry at least one PKU gene.

PKU occurs due to a deficiency or absence of the enzyme phenylalanine hydroxylase (PAH), which interferes with a person’s ability to metabolize or process the amino acid phenylalanine (PHE) into tyrosine, another amino acid. Amino acids, like PHE, are the building blocks of protein found in food and the human body. Consuming too much PHE from food can lead to a toxic build-up of PHE in the blood and brain of a person with PKU. Without treatment, this buildup of PHE will cause irreversible brain damage.

Presently, there is no cure for PKU, but it can be managed effectively with proper diet and special nutritional formulas designed for persons with PKU.  View products.

Incidence of PKUAutosomalRecessiveInheritance

In order for an individual to have PKU, both parents must pass along their PKU gene to their child. When both parents are carriers of PKU, there is 1 in 4 chance with each pregnancy that the child will have PKU, 1 in 2 chance of the child being a carrier, and 1 in 4 chance that the child will neither have PKU nor be a carrier.

It is estimated that one out of 10,000 live births has decreased PAH activity(1). Autosomal Recessive Inheritance Normal Gene Carrier Non Carrier Carrier Carrier PKU Carrier PKU Gene Phenylketonuria (PKU) *Phenotype- observable traits, outward appearances, development or behavior.

Newborn Screening for PKU

Newborn screening for PKU began in the US and Canada in the 1960s. It is important that an infant is diagnosed and managed with diet within days after birth to prevent permanent negative effects from PKU.

Nutricia is proud to offer the largest variety of great tasting formula options for people with PKU.  

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Learn more online at MedicalFood.com or contact us at (800) 605-0410 for free product samples.

Your metabolic dietitian will help you decide which products are right for you.  PKU formula must be used under medical supervision.

Nutricia is a proud supporter of PKU Awareness Month and the National PKU Alliance

Nutricia is a proud supporter of PKU Awareness Month and the National PKU Alliance

References
1. Vockley J, Andersson HC, Antshel KM, et al. Phenylalanine hydroxylase deficiency: diagnosis and management guideline. Genet Med. 2014;16(2):188-200.

PKU Periflex Junior Plus – Tips for Transition

Nutricia recently launched PKU Periflex® Junior Plus, a new addition to the Periflex family, with the goal of providing the best in PKU nutrition to your child. Towards this goal they have improved Periflex® Junior based on latest medical and scientific knowledge.

PKU Periflex Junior Plus - PKU Formula for Children

Available in Berry, Orange, Plain and Vanilla

Learn more about PKU Periflex Junior Plus

PKU Periflex Junior Plus has been improved to now provide DHA and Fiber for your child

  • DHA is an omega-3 fatty acid found to be lacking in the typical PKU diet
  • Nutricia’s own patented Multi-Fiberblend was added to help support your child’s overall gut health.

DID YOU KNOW IT CAN TAKE SEVERAL ATTEMPTS FOR A CHILD TO GET USED TO A NEW FOOD OR PKU FORMULA?

For some kids, a change in formula can be challenging. Some kids may need to try new foods/formula many times before acquiring a taste for it. So please be patient if that is the case with your little one.

To help we have created the PKU Periflex Junior Plus Activity Book.

PKU Formula Activity Book

Help your child transition to PKU Periflex Junior Plus with this fun, interactive activity book

Call 800-605-0410 to request a FREE Copy

Be sure to talk to your dietitian or clinic about a transition plan. They can provide a plan that will guide you step by step to make a slow and stead move to the new product by mixing  the new product and current product together to aid your child in making a successful change to PKU Periflex Junior Plus.

Request a Sample Now

Written by Linda Leuffgen, RD – Medical Affairs Associate, Nutricia North America