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Category Archives: Products for PKU

PKU & Pregnancy – 1st Trimester

Congratulations on your pregnancy! These are exciting times. Don’t forget: working closely with your clinic is important before, during and after pregnancy. Your clinic can provide the best guidance for you and your baby.

Once your blood phenylalanine (PHE) levels are well-controlled and you become pregnant you enter the first of three trimesters associated with pregnancy. Each trimester will have its own challenges and rewards.

In the 1st trimester, you will gain anywhere from 1-5 pounds. Your baby will grow from the size of a tiny poppy seed to about the size of lemon. Some women report feeling nausea during their first trimester and having difficulty keeping food down; especially in the morning hours.

Despite these challenges it is extremely important to drink your formula as it provides PKU friendly protein and general nutrition, which is essential for you and your baby.

If nausea and vomiting strikes, here are some general tips to help:

  • Try eating just the foods you enjoy most
  • Cold foods are sometimes better tolerated than hot foods
  • Avoid taking any vitamin/mineral supplement on an empty stomach
  • Avoid an empty stomach with small frequent snacks every 2 hours during the day

If nausea and vomiting strikes, here are some tips if the volume of PKU formula is an issue:

  • Ask your metabolic dietitian if a lower volume PKU formula is appropriate for you
  • Divide your current PKU formula into small frequent portions throughout the day

If nausea or vomiting is triggered by formula smell, here are some tips:

  • Ask your metabolic dietitian if you can try a PKU formula with less of a smell
  • Drink your current formula through a straw from a container with a cover to avoid smelling the formula while drinking

Some women also report constipation in their 1st trimester. Here are some tips to help:

  • Focus on fruits and vegetables that are high in fiber and low in PHE
  • Be sure you are drinking enough fluid / water

Request a Nutricia Maternal PKU Starter Kit for more helpful tips and tools to get you ready for this next stage in life.

All products shown are medical foods for the dietary management of Phenylketonuria (PKU) and must be used under medical supervision. Please consult your metabolic healthcare professional prior to making any changes to your PKU diet.

© 2019 – Nutricia North America

PKU & Pregnancy – Preconception

The journey to motherhood, when you have Phenylketonuria (PKU), should begin with your metabolic clinic. It is essential to work with your clinic before, during and even after pregnancy. Only your clinic can provide the best guidance to ensure the best outcome for you and your baby. They will work with you to ensure well-controlled blood phenylalanine (PHE) levels prior to pregnancy and throughout your pregnancy to prevent the negative effects of elevated PHE.

Studies in maternal PKU (MPKU) have shown uncontrolled blood PHE levels during pregnancy can cause the following outcomes for the baby:

  • Microcephaly (small head size)
  • Intellectual disability
  • Behavioral issues
  • Congenital heart defects (CHD)
  • Low birth weight and reduced length for age

Keeping your PHE levels within recommended range will help protect your baby from these risks.

Steps to getting PHE levels in the recommended range:

Find low-PHE recipes at medicalfood.com/recipes

Recommit yourself to the low PHE diet

  • Explore vegan recipes with the plant-based protein ingredient omitted (such as nuts, soy, tofu, etc.)
  • Change regular bread, rice and pasta to low protein versions, such as Nutricia’s Loprofin low protein food line

Find a PKU formula you enjoy

  • Nutricia offers the widest range of PKU formula options. You are sure to find one that meets your personal taste and needs. Check out Nutricia’s formula options here.
  • Create a plan and stick to it – this will help to make sure you take all your recommended formula each day at scheduled times.

Make a new routine

  • Regular blood samples (blood spots) will let you know when your PHE levels are in the ‘safe-range’ for pregnancy. Set a reminder on your calendar or cellphone to send your blood spots to your clinic on a regular basis (as instructed by your clinic).
  • Meal planning in advance will help make food shopping and new dining habits easier.

Get connected

For more helpful tips and tools to help get you ready for this next stage of life, request a Nutricia Maternal PKU Starter Kit.

All products shown are medical foods are for the dietary management of Phenylketonuria (PKU) and must be used under medical supervision. Please consult your metabolic healthcare professional prior to making any changes to your PKU diet.

© 2019 – Nutricia North America

Boo! A Simple Low Protein Halloween Treat

A not-so-spooky recipe for gatherings and parties this season

Free ground shipping on all orders over $30.

Happy October! Halloween will be here in a flash, and our team at Nutricia wants to share with you and your family a simple low protein Halloween snack: marshmallow squares made with our Loprofin Cereal Loops!

Nutricia Loprofin Cereal Loops are perfect for a satisfying low protein breakfast, as well as special treats like this! Available at MedicalFood.com.

With a delicious base recipe and endless decoration possibilities, this treat is ideal for Halloween gatherings and trick-or-treat parties where you and your family would like to include a low protein option.

Click here for our low protein cereal marshmallow treat recipe and nutrition information. These treats are frighteningly simple to make because the recipe calls for just 3 ingredients! As an added bonus, the recipe is ready in a matter of minutes.

With the base recipe complete, add some Halloween flair:

Fun candy eyes*:

*Candy eyes were purchased at a party store and contain 0 g protein per 1 tsp serving size, per Nutritional Facts label on the back of the package.

You can also insert Halloween cupcake toppers into the squares if you don’t want to add any additional food ingredients to the treats. Themed cupcake toppers can be found in party stores and even grocery stores during this season.

Lastly, adding simple paper decorations to your plate is another easy way to get into the Halloween spirit:

Enjoy, and Happy Halloween to you and yours from the Nutricia team!

Check out our Facebook page for more fun recipes and gathering ideas!

Loprofin brand cereal Loops is a medical food for the dietary management of inherited metabolic disorders, renal or liver failure requiring a low protein diet, and other medical conditions where a low protein diet is indicated. Must be used under medical supervision.

© 2019 Nutricia North America

Proud Moments for the Mullen Family

Brady and Quinn drink PhenylAde® GMP Drink Mix and start owning their PKU diets

Do you remember the moment you got the call about your child having an inborn error of metabolism?

In this video, Allyson Mullen shares her heartfelt story about that moment. Her sons Brady and Quinn received classical Phenylketonuria (PKU) diagnoses, which scared Allyson at first. Allyson opens up about what she’s learned as a parent and how Brady and Quinn have started taking on responsibility for their PKU management.

Allyson also shares why the Mullen family made the move to PhenylAde GMP Drink Mix for the boys’ PKU formula. Spoiler Alert: Brady actually called this formula “delicious,” and mom Allyson loves it because the formula contains glycomacropeptide (GMP). GMP is made from a whole protein source, and Nutricia’s PhenylAde GMP Drink Mix has a creamy, mild vanilla flavor with a smooth drinkable texture. It is also available in an original plain flavor.

Watch now to hear more about Allyson Mullen’s proud moments and why her boys love PhenylAde GMP Drink Mix.

Brady and Quinn Mullen made the move to PhenylAde GMP Drink Mix for their PKU formula.

Will your family give it a try?

PhenylAde GMP Drink Mix is a medical food for the dietary management of proven Phenylketonuria (PKU) and must be used under medical supervision.

Always consult a metabolic healthcare professional prior to making any diet changes.

© 2019 Nutricia North America

Back to School Interview with Heather Bomar

Heather, right, with daughter Ellis

Tips and wisdom from a parent of a PKU 7th grader

“I feel like I’m pulled in four different directions all summer!” says Heather Bomar of Brentwood, Tennessee, in describing her busy but fun summer season. Her four children, including 12-year-old Ellis who has classical Phenylketonuria (PKU), do a variety of activities over the summer. This means Heather spends much of the warmer months making sure they get where they need to go. 

In thinking about the back-to-school season, Heather reflects that the new year brings a new routine:

“The kids actually love the new schedule and seeing who’s in their classes,” shares Heather. The new routine also helps keep Ellis’ phenylalanine (PHE) levels in check, since the school year means set meal times and fewer impromptu gatherings that may or may not have low protein food options.

With Ellis heading into 7th grade, Heather is very familiar with back-to-school planning that works well for both Ellis and the family:

Download our Teachers and School Nurses PKU Education Guide to hand to your child’s teachers or use during parent-teacher meetings! Check out other PKU educational materials on the Nutricia website.

First, Heather meets with Ellis’ new teacher at the beginning of each school year to run through the basics of Ellis’ condition and diet. Second, she recommends co-creating a plan with the teacher, if necessary, to provide the best chance of success for a student with PKU, such as the student sitting in one of the least distracting places in the classroom. 

One of the most top-of-mind topics for parents of children with PKU is school lunch. The Bomars send Ellis to school with lunches packed at home. It’s a system that works for Ellis and the family. For her PKU formula, Ellis drinks PhenylAde® GMP Mix-In formula at school. When asked about snacks and lunch items, Heather responds without hesitation that Ellis’ favorite is “anything that she can dip in Ranch dressing!” Examples include celery, carrots, and peppers.

Ellis drinks PhenylAde GMP Mix-In formula at school. Will your family give it a try this year?

Other lunch favorites of Ellis’ include dried fruit, especially store-bought freeze-dried strawberries and apples. After school or at home on the weekends, Ellis enjoys low protein crackers smeared with butter and salt, a snack that Heather sometimes shares with her daughter as they catch up and talk about Ellis’ middle school, which Heather also attended!

Outside of lunchtime and PKU management, Ellis’ 7th grade year will revolve around establishing her sense of self: 

“Ellis loves school and has a good group of friends,” reflects Heather, “and she’s focused on finding her identity in things outside of PKU.”

As advice to other parents raising children with PKU, Heather takes a step beyond day-to-day food prep and considers the full parent-child relationship: “Stick with them through the highs and lows,” says Heather, “Keep up open conversations.”

… And don’t forget the Ranch dressing!

Read on for 10 More Low Protein Lunch Tips for School:   http://www.lowproliving.com/lunchtips/

PhenylAde GMP Mix-In is a medical food for the dietary management of proven Phenylketonuria (PKU) and must be used under medical supervision.

Always consult your metabolic healthcare professional prior to making any changes to your diet.

© 2019 Nutricia North America

What is GMP?

You’ve likely seen ‘GMP’ on a Phenyketonuria (PKU) or Tyrosinemia formula label or heard about it through your dietitian. But what exactly is it and why is it getting so popular?GMP can be used as a protein source for PKU and Tyrosinemia formulas. GMP, short for glycomacropeptide, is a peptide – a type of short protein. Peptides typically consist of shorter chains of amino acids, whereas true proteins are larger and more complex structures.

GMP is a byproduct of the cheesemaking process. Cheese is made from milk and contains intact protein. Milk consists of two types of proteins: casein and whey. During the cheese making process, the whey is separated from the casein; the casein part is what is used for cheese, the whey part is used for other purposes. GMP is found in the whey portion and must be filtered out to be used as an ingredient in formulas.

Contrary to other proteins, pure GMP does not contain phenylalanine (PHE), tyrosine (TYR) and a couple of other amino acids. That’s why it is a suitable protein source for PKU and Tyrosinemia formulas. However, through the process of isolating GMP from the whey part of the milk, some very small amounts of PHE and TYR cannot be filtered from the actual GMP and are part of the GMP ingredient used in PKU and Tyrosinemia formulas.

GMP by itself lacks certain amino acids that are important for growth and development. These amino acids must be added to the formulas so that PKU and TYR formulas are appropriate for individuals with PKU or Tyrosinemia. That’s why you see GMP and free amino acids listed as ingredients on your PKU and Tyrosinemia formula label.

You may have noticed slight variations in the PHE content when comparing GMP formulas (for example, between 10‐18 mg PHE per 10 g protein equivalent). Healthcare professionals have told us, that the differences are so small that they are clinically not relevant, and studies support this. This means that if a GMP‐based product is appropriate for someone with PKU or Tyrosinemia, the slight differences in PHE content are not important.

GMP is still a growing concept, but several studies support that GMP‐based products are safe and appropriate for most individuals with PKU or Tyrosinemia. GMP‐based products have a milder taste, and that milder taste is often preferred over amino acid‐based products. Finding a formula you or your child like is very important as that can certainly help with diet adherence. In addition, a small number of studies also report that patients feel fuller when consuming a GMP‐based formula.

A small number of clinical studies are also looking into other benefits of GMP‐based products in metabolics. However, the results of these studies are inconclusive. More research is needed to provide definite answers.

For some people with PKU or Tyrosinemia, the amount of PHE in GMP‐based formulas may be too high. Rest assured that formulas that are based 100% on amino acids (with no GMP) provide you or your child with all the nutrients needed for proper growth and development, including important vitamins and minerals for bone health. But of course, your dietitian can advise you on which formula is best for you or your child.

Want to find a GMP‐based formula? You’ve come to the right place!

Check out the variety of GMP‐based formulas that Nutricia has to offer: click on a product above  and read our blog on GMP‐based products from Nutricia.  READ NOW

Always talk to your dietitian before making any diet changes – and contact us if you have any questions about metabolic formulas. Visit www.MedicalFood.com for more information.

Written by: Ulrike Reichert, MS

Director Medical Affairs Keto/Metabolics Nutricia North America

 

 

PhenylAde GMP READY, PhenylAde GMP Drink Mix, and PhenylAde GMP Mix-In are medical foods for the dietary managment of proven Phenylketonuria (PKU) and must be used under medical supervision.  TYR Lophlex LQ is a medical food for the dietary management of proven Tyrosinemia  and must be used under medical supervision. 

 

Nutricia offers variety and choice in GMP‐based products:

At Nutricia, we are dedicated to providing more choices to more people. We have recently added new GMP‐based products to our portfolio. To read more about what GMP is, click HERE.

For those of you who want an overview of what is available in GMP‐based products from Nutricia, we made this quick reference guide. Get inspired to find your favorite one!

GMP‐based products for Phenylketonuria

(click the product box to learn more)

GMP‐based products for Tyrosinemia

Get READY for a Difference You Can Taste! No Mixing! GMP‐based powder to create the “Ultimate PKU Protein Shake” Virtually tasteless and odorless to mix in beverages or semi‐solid food Mild taste to mix in beverages or semi‐solid food

 

Always talk to your dietitian before making any diet changes – and contact us if you have any questions about metabolic formulas. Visit MedicalFood.com for more information.

Your Nutricia Metabolics Team

 

 

 

 

 

PhenylAde GMP READY, PhenylAde GMP Drink Mix, and PhenylAde GMP Mix-In are medical foods for the dietary managment of proven Phenylketonuria (PKU) and must be used under medical supervision.  TYR Lophlex LQ is a medical food for the dietary management of proven Tyrosinemia  and must be used under medical supervision. 

 

Are you READY?

Are you READY?

New at Nutricia is PhenylAde® GMP READY, a ready‐to‐ drink PKU formula, providing 10 g protein equivalent and 110 kcal in one drink box (8.5 fl oz). It is also the only GMP‐ based formula with both DHA and EPA, two important omega‐3 fatty acids missing in the PKU diet.

PhenylAde GMP READY:

  • Offers an enjoyable, neutral flavor with a smooth texture for easy drinking

  • Contains GMP, which is made from an intact protein source and is naturally low in phenylalanine.   Click HERE to learn more about GMP.

  • Provides an excellent source of both calcium and vitamin D, two nutrients that help build and maintain strong bones and teeth

A ready‐to‐drink formula can make your life so much easier: from grabbing it in the morning for your breakfast drink to throwing it in the lunch bag for school or work or when you travel. We all have busy lives, and PhenylAde GMP READY is here to provide great nutrition in a convenient drink box.

Take the taste challenge as some of your fellow PKUers have done and let us know your thoughts!

GET READY TODAY!

Always talk to your dietitian before making any diet changes – and contact us if you have any questions about metabolic formulas. Visit MedicalFood.com for more information.

Your Nutricia Metabolics Team

 

 

 

PhenylAde GMP READY is a medical food for the dietary management of proven Phenylketonuria (PKU) and must be used under medical supervision.

Get Ready for Summer with PKU Lophlex LQ!

Summer is one of the best season!  Long days, fun adventures, amusement parks and the warm sun are just a few reasons summer is such a great time of the year.

When you have PKU, you also need to think about how you will transport and drink your PKU formula when out for a full day.

Imagine you could have a great tasting PKU formula that you could easily drink when:

– Mountain Biking
– Canoeing with Friends
– At an Amusement Park
– Hiking or Camping
– Vising Family or Friends
– Hanging Out by a Lake

 

Don’t imagine it any longer!

Try PKU Lophlex LQ, a great PKU formula for summer. Each ready-to-drink pouch is protein packed with 20 g of protein equivalent and only 120 calories. Lophlex LQ are low volume and ready-to-drink which is great for life on-the-go.

Plus, it is the only low volume, ready-to-drink PKU formula made with real fruit juice* from concentrate for a refreshing taste on a hot summer day.

The only question is …

Post your on-the-go PKU Lophlex LQ photo on Instagram!  #PKU Summer

 


Try PKU Lophlex LQ Today!

✓ Low Volume
✓ Only 120 Calories
✓ Quick & Easy to Drink

      REQUEST A SAMPLE 3-PACK

Available in Mixed Berry, Juicy Orange and Juicy Tropical


*Juicy Orange contains 45.5% juice. Mixed Berry Blast contains 44.1% juice. Juicy Tropical contains 28.4% juice.

PKU Lophlex LQ is a medical food for the dietary management of proven Phenylketonuria (PKU) in individuals over 4 years of age. Must be used under medical supervision. Consult your metabolic clinic prior to making any changes to your metabolic diet.

Copyright 2018 Nutricia North America

Drink It How You Like It

Turn What You Like Into PKU Formula with PhenylAde® GMP Mix-In

mix-in-full-art

mix-in-suggestions

6300143Virtually Tasteless and Odorless

#DrinkItHowYouLikeIt

PhenylAde GMP Mix-In is a medical food for the dietary management of proven Phenylketonuria (PKU) and must be used under medical supervision. Always consult your metabolic healthcare professional prior to making any changes in your PKU diet plan.