*Always talk to your metabolic healthcare professional prior to making any changes to your PKU diet.
Phlexy-10 Tablets are a phenylalanine-free medical food in tablet form, containing a mix of other essential and non-essential amino acids and small amounts of carbohydrate and fat. For the dietary management of proven Phenylketonuria (PKU), suitable for individuals over 8 years of age, including pregnant women and women of childbearing age. Must be used under medical supervision. Does not contain vitamins and minerals; must be combined with an appropriate vitamin and mineral supplement when taken as primary source of PKU medical food.
Meet Lorenzo Mennucci. The Mennucci family began making Loprofin Pasta almost 50 years ago in Tuscany. It is now in its fifth generation and is managed by Lorenzo Mennucci. In 1877, Giuseppe Mennucci started making pasta in a small grocery store in the countryside of Tuscany. At that time, the process of making and drying the pasta was carried out in the courtyard under the sun. This all nearly ended during the Second World War, when the company was bombed and partially destroyed. After the bombing, the Mennucci family was quick to rebuild the factory. During the rebuilding process, all pasta machines that were not destroyed were moved into local homes near Tuscany to maintain the production of pasta.
The Mennucci family are very passionate about using the highest quality of ingredients which are mainly sourced from Italy. There are only four ingredients in low protein pasta which are mainly starches; corn, potato, rice and coloring (annatto). Lorenzo believes that when there are so few ingredients in a product it is important that you use the highest quality of ingredients.
The main difference in the production of low protein pasta and ordinary pasta is that gluten is the protein that binds the dough in ordinary pasta. For low protein pasta, steam is used instead to bind the starches together to make a dough. Low Protein Pasta is made using spring water that comes from the Tuscan mountains.
See for yourself where our Loprofin Pastas are made in this video of the Mennucci family!
View recipes made with Loprofin Low Protein Pasta at MedicalFood.com/Recipes
Loprofin Mix is an all‐purpose, low protein baking mix, great for cooking and home‐made pastries. A packet of yeast is provided in each box, making baking easy, especially bread. Nutricia also offers Loprofin Chocolate Cake Mix, great for any chocolate cake or muffin recipe. Tasty recipes, such as breads, naan, cupcakes, gingerbread and many more can be found here!
Loprofin Mix is a great substitute for Wel‐Plan Baking Mix, which is unfortunately no longer available. Several low protein expert chefs shared that they substitute Wel‐Plan Baking Mix with Loprofin Mix at a 1:1 ratio. For example, if a recipe asks for one cup of Wel‐Plan, you would use one cup of Loprofin Mix. We have also test‐baked a few low protein bread recipes from “Apples to Zucchini”, a cookbook by Virginia Schuett and Dorothy Corry, and confirmed that Wel‐Plan can be substituted at a 1:1 ratio with Loprofin Mix for many bread recipes. Check out these recipes with Loprofin Mix that work for making bread – with or without a bread machine!
Many of you relied on Maddy’s Homestyle baking mixes as convenient, quick mixes. We developed recipes where you can use the Loprofin Mix to make the same baked goods. New Loprofin recipes such as, sugar cookies, banana bread and blueberry muffin, to list just a few can be found here.
Look out for our future blogs on holiday cooking and baking, as well as making the low protein kitchen convenient, quick and tasty!
The holidays can be an exciting time of year. However, they can be a bit challenging for someone on a restricted diet as most festivities center around food. This blog focuses on tips for managing a restricted diet during the holiday season.
The most important thing to do is plan ahead. The more you know in advance, the better you can plan.
Here are some questions to ask yourself:
Where will I be spending the holidays and how long will the trip be?
Do I have enough formula so I do not run out while away over the weekend?
Am I dining at home or at someone else’s home?
Will I be preparing the food or will someone else?
Once you know more about what your day/weekend will consist of, you can make a plan.
One key thing is to plan the menu in advance. If you are not dining at home, but at a friend’s or relative’s home, it will be important to ask what is being served, then…
Ask if you can bring a side dish (one that is suitable for you, but enough for everyone to share).
Let them know about your dietary needs so they can omit or serve items on the side that are not low protein friendly, like cheese or bread crumbs.
See if you can access the kitchen to re-heat or make additional low-protein items for the holiday meal.
Many traditional holiday favorites can be modified to reduce the protein while still keeping the taste and texture you and others love.
Here is a simple recipe for a popular dish with small changes to lower the protein content – this dish is sure to become a family staple at your holiday meal:
Reduced Protein Mashed Potatoes
2 cups (248 g), Cauliflower, florets
2 cups (312 g), White potato, peeled and cut into pieces
1 cup (156 g), Parsnips, peeled and cut into pieces
¼ cup (56 g), Non-dairy creamer, liquid
2 tablespoons (28 g), Margarine, dairy-free
To taste (2-3 g), Salt and pepper
Boil potato and parsnip in a large pot until they begin to soften.
Add cauliflower and continue to cook until soft and tender.
Place all ingredients in a food processor and blend until smooth.
Salt and pepper to taste.
Makes 7 servings
13.8 g protein
709 mg leucine
499 mg phenylalanine
337 mg tyrosine
2 g protein
101 mg leucine
71 mg phenylalanine
48 mg tyrosine
End your holiday meal on a sweet note with this low protein dessert. This is a dish everyone at your holiday gathering is sure to enjoy!
Easy Pumpkin Pudding (recipe developed by Sarah Marshall)
1 fluid ounces Water
7 fluid ounces Coconut Milk (full fat, canned coconut milk required to get pudding-like consistency)
6 each Whole pistachios (for flavor – to be strained out later)
½ tablespoon Brown sugar
¼ teaspoon Pumpkin pie spice (or blend cinnamon, ginger and nutmeg)
½ teaspoon Vanilla flavoring
½ cup Loprofin Rice
In a small saucepan, add 1 oz water & 7 oz coconut milk and 6 pistachios.
Bring to a boil. Immediately when it begins boiling, add brown sugar, vanilla and pumpkin pie spice and stir.
Add Loprofin Rice. Stir. Cover and lower heat to simmer covered for 10 minutes.
Once rice is cooked remove pistachio pieces.
Serve warm or cold.
Makes 2 servings
4.1 g protein
306 mg leucine
207 mg phenylalanine
124 mg tyrosine
2 g protein
153 mg leucine
104 mg phenylalanine
62 mg tyrosine
And most of all…
Holidays do not have to be all about food. Make your holidays memorable with family traditions, such as a family football game or a checkers tournament.
For children with an inborn error of metabolism, Halloween celebrations can be tough since protein-containing candy and snacks tend to be the classic party staples. Additionally, these celebrations can be scary on parents as they want their children to fully enjoy in the festivities while maintaining their dietary restrictions.
Here are a few tips, resources, and recipes to help make Halloween fun while staying on a diet low in intact protein:
Speak with teachers or other parents about what your child can and cannot have at Halloween parties or school
Also talk with your child about the importance of staying on diet and remind them to check with you to determine if a particular food or candy is
Now to the Fun Stuff:
Get creative with Halloween Have non-food treats to hand out at home or at school. Think dollar store toys, stickers, party favors, and coloring books.
Plan an alternative activity to trick-or-treating, such as Halloween slumber party, game night, craft party, or a scavenger
Supply low-protein treats for your child’s Halloween parties and festivities so he/she has something to enjoy and doesn’t feel left out – View Halloween Cupcake Recipe
Consider having a “swap-party” where your child can swap candies he/she cannot have for “allowed” This way everyone gets what they want!
Make your child’s metabolic formula festive! Serve it in a Halloween- themed cup, use fun straws, or add some orange food
Post Your Formula ‘Dressed-Up’ for Halloween and TAG Nutricia!
Halloween Low Protein Cupcakes
Surprise a special someone or treat yourself to a Halloween cupcake. These cupcakes are made with Loprofin Baking Mix. They are easy to make and great for at home, work or parties.
Cream together margarine and sugar until light and fluffy
Add LoprofinBakingMix, egg replacer, and baking powder into the creamed mixture and mix well
Add water, vanilla extract and orange food coloring gradually, mix until smooth
Spoon batter into paper cups filling each cup about 2/3 full and bake for approximately 10-15 minutes
Let cool on a baking rack
Decorate with frosting and candy corn
Note: Any additional frosting or decorations may add additional protein, phenylalanine, leucine or calories, be sure to read labels and account for any topping or decorations.
All Nutricia products shown are for the dietary management of inborn errors of metabolism and must be used under medical supervision. Please consult your metabolic healthcare professionals prior to making any changes to your diet.
Now is a great time to re-commit to better PKU diet management. Nutricia has a team of professionals who can assist you, or your loved one, get back on-diet.
Our help includes personalized support ranging from finding the right PKU formula, to resetting your low protein kitchen, and more. Our Diet-For-Life Care Coordinator can also lend an extra helping hand.
In addition, Nutricia can review your insurance and answer any questions you may have about formula coverage. Schedule a one-on-one insurance review today. Coverage@Nutricia.com
You can do it. You are not alone!
You can do it – and Nutricia is here to help.
• Help you learn about new PKU formula options
• Provide more information about PKU and returning to diet
• Connect you with a metabolic clinic or a return to diet specialist
• Review your insurance plan for PKU formula coverage
• Share recipes and low protein cooking tips
Don’t Wait Any Longer!
DietforLife@Nutricia.com or call 800-605-0410
NOTE: All PKU formulas must be used under medical supervision. Always consult your metabolic healthcare professional prior to making any changes in your PKU diet plan.
Posted by: Sandy Simons, MA, RD, CHES
Sandy is a Registered Dietitian and Certified Health Education Specialist. She received her graduate training at Columbia University’s Teacher College in New York. She has been working on the industry side of metabolic nutrition for the past 14 years and is often seen at patient events around the country.
Satisfaction from food or a meal is something everyone wants. Although many foods may be restricted or limited on a low protein diet, you do not have to compromise taste. Selecting the foods you eat involves a variety of factors. We choose foods based on taste and smell, in addition to texture, sight and culture.
To make the most of your meal, begin by identifying what you crave, like spicy, sweet, crunchy or salty. This will make your meal more satisfying.Here are some tips to help you make the most of your meal.
Spicy:Add seasonings that can add a kick. For example, add cracked pepper, crushed red pepper or hot sauce to steamed vegetables to give a familiar item a new twist.
Sweet & Tangy:Satisfy your sweet and tangy craving with grilled pineapple topped with BBQ sauce on a low protein bun. You can also add mandarin oranges and Italian dressing to a garden salad for added flavor and tang.
Crunchy: With a little creativity you can add a snap to any dish. Make your own salad croutons with low protein bread. Season them in a variety of ways by using garlic powder, cayenne pepper or Italian herbs depending on your personal desire for savory or spice. Another great way to add crunch is to include raw vegetables, like cucumbers or carrots slices to a salad or sandwich.
Salty: Salt is among the most popular taste craving. Although highly desired, salt is an ingredient to be used in moderation. A little bit goes a long way. To satisfy your craving for salt, try slicing fresh potatoes very thin and sprinkling with garlic and a touch of sea salt. Bake them until crisp for a satisfying addition to your meal or snack.
Smooth and Creamy:Create your own creamy low protein dip with your favorite seasonings for a flavorful way to enjoy Low Protein Crackersor fresh cut vegetables. You can also include a sweet treat at the end of your meal to help satisfy your need for something smooth and creamy.
Beat the heat and satisfy your appetite with a cool summer salad!
Summer is the perfect time to enjoy fruits and vegetables at the peak of freshness. A make-your- own salad station makes a great addition to any cookout or pool party. You can also spice up a green garden salad by bringing along your favorite toppings and low protein dressing.
Try these themed salads for a fresh take on the usual bed of greens:
Fajita Salad: Create a colorful nutrient-packed meal by topping your salad greens with sautéed red and green bell peppers, onions and zucchini.
Mushroom Salad: Portobello mushrooms sautéed in fresh garlic or grilled can turn an ordinary salad into a savory meal.
Fruit Salad: Add diced apple, dried cranberries, diced peaches and grapes over greens. Toss with a light vinaigrette dressing for a sweet and tangy summer treat.
Mexican Salad:Spice up your salad with finely diced black olives, onions, cucumbers and tomatoes. Add jalapeños and salsa for an extra kick.
Roasted Vegetable Stacker: Toss coarsely chopped zucchini, eggplant, red pepper and onion in garlic oil and roast until tender. Serve piled high over a bed of salad greens.
Ratatouille Salad: Stew diced eggplant, olives, zucchini, garlic and onion in a broth made of tomato puree mixed with water. Allow to cool. This tasty topping can be served over greens or chilled low protein pasta to create a unique summer salad.
Turn your summer salad creation into PKU friendly protein source
Just mix 1 pouch (12.5g) of PhenylAde® GMP Mix-In(PKU formula) into 2 Tbsp of salad dressing for 10g of Protein Equivalents
The holiday season is full of fun, friends and family time. It can also be challenging to those following a special diet, but with advance planning you can enjoy the festivities without overindulging.
Don’t forget your formula! Plan to have it between meals or drink before a meal to help prevent exceeding your prescribed diet.
Make a Plan. Check out your food options before filling your plate. Make sure not to go over your daily natural protein allowance.
Bring a dish. If you are going to have the holiday meal at a friend’s or relative’s home, bring a low protein friendly dish everyone can enjoy. This way you will be certain to have food you like, but also share with others.
Below are some suggestions and tips for creating a holiday menu that will help you to stay within your recommended protein intake.
Soups & Appetizers
Start with a variety of fresh raw vegetable crudités with a low protein dip or salsa.
Be sure soups are vegetable based and do not include hidden animal protein or dairy.
Oven roast a variety of vegetables tossed with olive oil and garlic or other low protein seasonings for a flavorful side dish that everyone can enjoy.
Serve steamed vegetables with sauce on the side. This will allow you to choose how much, if any sauce, to add.
Make some minor changes to some old favorites. Reduce the protein content of mashed potatoes by blending potato with parsnip, cauliflower, non-dairy creamer and dairy-free margarine for that real mashed potato taste with less total protein. View Recipe
Low protein stuffing is easily made by substituting cubed low protein bread as your main ingredient. Use vegetable broth and dairy-free margarine for moisture. Add celery, onions, diced apples and your favorite seasonings for a delicious combination.
Save Room for Dessert
There are many delicious desserts that can take center stage after the meal. Try the following:
Home-made holiday cookies. Cookies can be the focus of a family activity. Bake Maddy’s Homestyle Sugar Cookies in advance either as drop cookies or rolled and cut into holiday shapes.
Purchase a variety of low protein frosting and sprinkles (choose holiday shapes and colors) and let everyone take part in the decorating fun.
For a special dessert, check out our low protein Holiday Cake. This delicious dessert tastes as good as it looks and will be a treat everyone can enjoy. View Recipe Here